Multisystemic Langerhans cell histiocytosis: case report
نویسندگان
چکیده
منابع مشابه
Multisystemic Langerhans cell histiocytosis in an adult
CT: computed tomography LCH: Langerhans cell histiocytosis PPAR-g: peroxisome proliferatoreactivated receptor-g INTRODUCTION The etiology of Langerhans cell histiocytosis (LCH), a mix between immune dysregulation, inflammation, and malignancy, remains unclear. In half of the patients, an oncogenic BRAF mutation is found. Because of the diversity of symptoms, the diagnosis of LCH, as defined by ...
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Langerhans cell histiocytosis (LCH) is a rare neoplasm defined as the proliferation of bone marrow langerhans cells, which is a kind of dendritic cells. The major pathological features of LCH are expression of CD1a and S100 as well as Birbeck granules. Its presentation can differ from a mild bone lesion to a multi-systemic evolved malignant neoplasm; however, the latter outcome is almost rare. ...
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Langerhans cell histiocytoses (LCH) are a rare group of disorders that comprise a large spectrum of diseases initially known as histiocytosis X. In this case report, we relate a case of LCH affecting the vulva of a 47-year-old female. The patient presented since 3 years with a vulvar lesion characterized by non-healing ulcers and a perineal granuloma on which she underwent surgery. Professional...
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A three and half year old boy with Langerhans' cell histiocytosis (LCH) formerly called as eosinophilic granuloma has been presented along with the desired treatment plan.
متن کاملLangerhans Cell Histiocytosis: a Case Report
Langerhans cell histiocytosis is a disease which results from accumulation or proliferation of a clonal population of cells with the phenotype of Langerhans cells arrested at an early stage of activation that are functionally defi cient. The etiology and pathogenesis of the disorder are still unknown. There are ongoing investigations to determine whether it is a reactive or a neoplastic disease...
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ژورنال
عنوان ژورنال: Jornal Brasileiro de Patologia e Medicina Laboratorial
سال: 2016
ISSN: 1676-2444
DOI: 10.5935/1676-2444.20160066